Stockley I, Bell M J, Sharrard W J
Sheffield Children's Hospital, England.
J Bone Joint Surg Br. 1989 May;71(3):422-7. doi: 10.1302/0301-620X.71B3.2656718.
We report the results of using 83 expanding intramedullary rods in 24 children with osteogenesis imperfecta after a mean follow-up of five years three months. In all, 62% of the rods have expanded after one primary operation. Thirty-four additional operations were necessary; 11 for the correction of rotation or angulation deformities and 23 for revision of the rod or T-piece. All these revisions were successful. Complications were more frequent in children who required very small rods. Problems with Bailey-Dubow rods led to the development of the Sheffield rod system; 17 bones treated with these rods are included in the series. Before surgery only eight of the 24 children were able to walk but at review 20 children were walking, 15 without walking aids. Elongating intramedullary rods should be available to all children with osteogenesis imperfecta as they improve walking capability, reduce the number of fractures, prevent deformity and allow integration of the child into society.
我们报告了在24名成骨不全患儿中使用83根可延长髓内棒的结果，平均随访时间为五年零三个月。总体而言，62%的髓内棒在一次初次手术后实现了延长。还需要进行34次额外手术，其中11次用于矫正旋转或成角畸形，23次用于髓内棒或T形件的翻修。所有这些翻修手术均获成功。在需要非常小的髓内棒的患儿中，并发症更为常见。贝利-杜波髓内棒出现的问题促使了谢菲尔德髓内棒系统的研发；本系列纳入了17根使用该髓内棒治疗的骨骼。术前，24名患儿中只有8名能够行走，但复查时已有20名患儿能够行走，其中15名无需借助助行器。对于所有成骨不全患儿，均应提供可延长髓内棒，因为它们能提高行走能力、减少骨折数量、预防畸形并使患儿融入社会。
