Yasuda K, Matsui Y, Goda T, Sakuma M, Sakai K, Tanabe T
Nihon Kyobu Geka Gakkai Zasshi. 1989 Feb;37(2):355-61.
We experienced two cases of the thoracoabdominal aortic aneurysms with Marfan's syndrome. Case 1; The 31 year-old-woman was operated upon by Crawford's procedure, which includes reconstruction of renal arteries, superior mesenteric artery, and celiac artery using temporary shunt. Although she had been well for three years after the operation before she developed acute aortic dissection, she could not tolerate the Bentall's procedure on it. Case 2; The 37 year-old woman was operated upon for dissecting aneurysm (DeBakey IIIb). The procedure included replacement of the descending and abdominal aorta by Dacron graft. Four years after the operation, enlargement of residual false lumen had been observed, which caused its dehiscence just proximal to the abdominal aortic anastomosis. The Crawford's procedure, which includes reconstruction of renal arteries, superior mesenteric artery, and celiac artery using temporary shunt was employed for repair of the remaining thoracoabdominal aortic aneurysm. She is well now 5 months after surgery. We conclude that cardiovascular changes in patients with Marfan's syndrome must be observed carefully because of its high recurrent rate after initial surgery. The operation at proper time and a careful observation of cardiovascular changes will improve the prognosis.
我们遇到了两例患有马凡氏综合征的胸腹主动脉瘤患者。病例1:一名31岁女性接受了克劳福德手术,该手术包括使用临时分流器重建肾动脉、肠系膜上动脉和腹腔动脉。尽管她术后三年情况良好,但后来出现了急性主动脉夹层,无法耐受针对该情况的本特利手术。病例2:一名37岁女性因夹层动脉瘤(德巴基IIIb型)接受手术。手术包括用涤纶人工血管置换降主动脉和腹主动脉。术后四年,观察到残余假腔扩大,导致其在腹主动脉吻合口近端出现裂开。采用克劳福德手术,即使用临时分流器重建肾动脉、肠系膜上动脉和腹腔动脉,来修复剩余的胸腹主动脉瘤。术后5个月,她目前情况良好。我们得出结论,由于马凡氏综合征患者初次手术后复发率高,必须仔细观察其心血管变化。在适当时间进行手术并仔细观察心血管变化将改善预后。