Rebellato Priscila Regina Orso, Rezende Camila Makino, Battaglin Eveline Roesler, Lima Brunno Zeni de, Fillus Neto Jose
Faculdade Evangélica do Paraná, Curitiba, PR, Brazil.
An Bras Dermatol. 2015 Nov-Dec;90(6):909-11. doi: 10.1590/abd1806-4841.20153818.
Morbihan Syndrome is a rare entity with unknown etiology. It is clinically characterized by chronic erythematous edema on the face - especially in the middle and upper third of the face - and creates abnormal facial contours that are initially intermitent but become permanent with the development of the syndrome. The histopathology is nonspecific and its therapy is a major challenge due to poor response to the various treatment options. We present the case of a male patient with a five-month-history of disease.
莫尔比昂综合征是一种病因不明的罕见病症。其临床特征为面部慢性红斑性水肿,尤其是面部中上部,会导致面部轮廓异常,起初这种异常是间歇性的,但随着综合征的发展会变为永久性。组织病理学表现无特异性,由于对各种治疗方案反应不佳,其治疗是一项重大挑战。我们报告一例有五个月病史的男性患者的病例。