Aboutaam Alaa, Hali Fouzia, Baline Kenza, Regragui Meryem, Marnissi Farida, Chiheb Soumiya
Department of Dermatology and Venereology, Ibn Rochd University Hospital, Casablanca, Morocco.
Department of Anatomy and Pathology, Ibn Rochd University Hospital, Casablanca, Morocco.
Pan Afr Med J. 2018 Jul 26;30:226. doi: 10.11604/pamj.2018.30.226.14440. eCollection 2018.
Morbihan disease (MD) is a rare entity. Its nosography is unclear and its therapeutic management is difficult. We report a new case of MD. We report a case of a 51-year-old patient consulted in our department for a one year facial edema, erythema and papules reported by him, for which the patient was treated with cyclins, local and general corticotherapy, without improvement. The clinical examination found an important edema of the front and eyelids with an erythema of the cheeks covered with a few telangiectasias. The clinical, biological and histological findings lead to a diagnosis of Morbihan disease after excluding other diseases. Due to previous therapeutic failures, the patient was put on isotretinoin and furosemide with slight improvement. The particularity of our observation lies in the rarity and especially in the therapeutic difficulties encountered during this disease.
莫尔比昂病(MD)是一种罕见病。其疾病分类尚不明确,治疗管理也很困难。我们报告一例MD新病例。我们报告一名51岁患者,因自述面部水肿、红斑和丘疹一年前来我科就诊,患者接受了环磷酰胺、局部和全身皮质类固醇治疗,但无改善。临床检查发现前额和眼睑严重水肿,脸颊红斑,伴有一些毛细血管扩张。在排除其他疾病后,临床、生物学和组织学检查结果确诊为莫尔比昂病。由于之前治疗失败,患者开始服用异维A酸和呋塞米,症状稍有改善。我们观察的特殊性在于该病罕见,尤其是在治疗过程中遇到的困难。