Mironov N Yu, Mironova N A, Sokolov S F, Mareev Yu V, Shlevkov N B, Saidova M A, Stukalova O V, Golitsyn S P
Kardiologiia. 2015;55(8):86-96. doi: 10.18565/cardio.2015.8.86-96.
We report a case of bundle-branch reentrant ventricular tachycardia as a first and severe manifestation of myotonic dystrophy. Progressive cardiac conduction disturbances and cardiac arrhythmias are well-known features of myotonic dystrophy, although they are commonly found in late stage of disease in patients with established diagnosis. We review clinical manifestations, diagnostics, management, and prognostic value of cardiac involvement in myotonic dystrophy.
我们报告一例束支折返性室性心动过速作为强直性肌营养不良的首发严重表现。进行性心脏传导障碍和心律失常是强直性肌营养不良的众所周知的特征，尽管它们通常在已确诊患者的疾病晚期出现。我们回顾了强直性肌营养不良心脏受累的临床表现、诊断、管理及预后价值。
