Beebe Kathleen S, Ippolito Joseph A
Rutgers New Jersey Medical School, Newark, NJ 07101, USA.
Rutgers New Jersey Medical School, Newark, NJ 07101, USA
J Surg Case Rep. 2016 Jan 13;2016(1):rjv171. doi: 10.1093/jscr/rjv171.
Desmoplastic fibromas are rare, benign, locally aggressive bone tumors, which arise primarily in patients younger than 30 years old. Historically, even with greater functional loss, en bloc or wide resection of the tumors to prevent local recurrence has been the method of choice in treatment. This article discusses the presentation of a 10-year-old male who presented with a mass in the distal forearm, after reporting difficulty in pronation and supination. The patient was ultimately treated with wide resection and allo-arthrodesis with allograft. Post-operatively, the patient has exhibited excellent recovery, including normal range of motion at the shoulder and elbow, and ability to perform all activities of daily livings despite reduced grip strength compared with the contralateral side.
促结缔组织增生性纤维瘤是一种罕见的、良性的、具有局部侵袭性的骨肿瘤，主要发生在30岁以下的患者中。从历史上看，即使会造成更大的功能丧失，为防止局部复发而对肿瘤进行整块或广泛切除一直是首选的治疗方法。本文讨论了一名10岁男性患者的病例，该患者在报告旋前和旋后困难后，在前臂远端出现肿块。该患者最终接受了广泛切除和同种异体骨移植关节固定术。术后，患者恢复良好，包括肩部和肘部的活动范围正常，尽管与对侧相比握力有所下降，但仍能够进行所有日常生活活动。
