Yokoyama Shinya, Nagato Hisao, Yoshida Yuichi, Nagasaka Shigeo, Kaneda Kozo, Nishiwaki Noboru
Department of Cardiovascular Surgery, Kinki University School of Medicine Nara Hospital, 1248-1, Otoda-cho, Ikoma, Nara, 630-0293, Japan.
J Cardiothorac Surg. 2016 Jan 16;11:4. doi: 10.1186/s13019-016-0403-5.
Although repair of a supravalvular aortic stenosis (SVAS) can be performed with low mortality rates, surgery for the complex form of SVAS continues to be associated with a high incidence of residual stenosis.
The patient was referred to our hospital at 1 month of age and was diagnosed with aortic valve stenosis (AS) by using echocardiography. Cardiac catheterization revealed moderate AS, and subsequent left ventriculography revealed discrete stenosis of the sino-tubular junction and a narrowed proximal ascending aorta. We performed a reconstructive operation for such heart defects involving novel three-sinus and ascending aorta enlargement without aortic root transection in a 6-month-old boy.
Our novel three-sinus enlargement technique is suitable for treating each type of SVAS and is a useful method for a baby particularly less than 10 kg without disturbing the growth of the ascending aorta.
虽然主动脉瓣上狭窄（SVAS）修复术死亡率较低，但复杂型SVAS手术的残余狭窄发生率仍然很高。
该患者1月龄时转诊至我院，经超声心动图诊断为主动脉瓣狭窄（AS）。心导管检查显示中度AS，随后左心室造影显示窦管交界离散性狭窄及升主动脉近端狭窄。我们为一名6月龄男童针对此类心脏缺陷实施了重建手术，采用了新颖的三窦及升主动脉扩大术，未切断主动脉根部。
我们新颖的三窦扩大技术适用于治疗各类型的SVAS，对于体重小于10kg的婴儿是一种有用的方法，且不会干扰升主动脉的生长。
