Myers J L, Waldhausen J A, Cyran S E, Gleason M M, Weber H S, Baylen B G
Division of Cardiothoracic Surgery, Penn State University Children's Hospital, College of Medicine, Milton S. Hershey Medical Center, Hershey, PA 17033.
J Thorac Cardiovasc Surg. 1993 Feb;105(2):281-7; discussion 287-8.
Our experience with congenital supravalvular aortic stenosis dates from 1977 to 1991. Thirteen patients, aged 2 days to 38 years (mean 7.6 years, median 3.8 years), had surgical repair of the lesion. The preoperative peak-to-peak systolic gradients ranged from 25 to 110 mm Hg (mean 64 mm Hg). Four patients had trace to mild aortic insufficiency. Surgical repair was accomplished by several techniques that have evolved over time. There was one death in a 2-day-old neonate who also had severe hypertrophic cardiomyopathy. The 12 survivors had postoperative gradients of 0 to 30 mm Hg (mean 10 mm Hg) in the supravalvular region. The mean reduction in gradient was 48 mm Hg. A new technique employing all autologous aortic tissue is described.
我们治疗先天性瓣上主动脉狭窄的经验始于1977年至1991年。13例患者，年龄从2天至38岁（平均7.6岁，中位数3.8岁），接受了该病变的手术修复。术前峰-峰收缩期压差范围为25至110 mmHg（平均64 mmHg）。4例患者有微量至轻度主动脉瓣关闭不全。手术修复通过多种随时间演变的技术完成。一名2天大的新生儿死亡，该新生儿同时患有严重肥厚型心肌病。12名幸存者在瓣上区域术后压差为0至30 mmHg（平均10 mmHg）。压差平均降低48 mmHg。本文描述了一种采用全自体主动脉组织的新技术。
