Mironov Nikolay Yu, Mironova Natalia A, Saidova Marina A, Stukalova Olga V, Golitsyn Sergey P
Department of Clinical Electrophysiology, Russian Cardiology Research Center, Russia.
Department of Sonography, Russian Cardiology Research Center, Russia.
Case Rep Cardiol. 2015;2015:151269. doi: 10.1155/2015/151269. Epub 2015 Dec 15.
Cardiac involvement is a well-known feature of neuromuscular diseases. Most commonly cardiac manifestations occur later in the course of the disease. Occasionally severe cardiac disease, including conduction disturbances, life-threatening arrhythmias, and cardiomyopathy, with its impact on prognosis, may be dissociated from peripheral myopathy. We report a case of bundle branch reentrant ventricular tachycardia as primary manifestation of myotonic dystrophy and discuss associated diagnostic and treatment challenges.
心脏受累是神经肌肉疾病的一个众所周知的特征。最常见的心脏表现出现在疾病进程的后期。偶尔,严重的心脏疾病,包括传导障碍、危及生命的心律失常和心肌病及其对预后的影响,可能与周围性肌病无关。我们报告一例以束支折返性室性心动过速为强直性肌营养不良主要表现的病例,并讨论相关的诊断和治疗挑战。