Torres López A, Péramo Fernández F, Costela Villodres J L, Carlos García R
Rev Esp Anestesiol Reanim. 1989 Sep-Oct;36(5):286-7.
We describe the anaesthetic management of a 20 years old female with a Friedreich's ataxia for curettage of the uterus. After the premedication with thalamonal, diazepam and atropine the anaesthesia was induced with thiopental. Isoflurane and nitrous oxide were used for maintenance. We review the literature about this disease and its implications in anaesthesia. Anesthetic hazards to the patient with Friedreich's ataxia include potential risk of cardiac dysrhythmias and heart failure and also marked sensitivity to muscle relaxants. Respiratory complications and diabetes mellitus are other main problems in postoperative period. We conclude that this patients should be careful monitored specially cardiovascular function and neuromuscular transmission during and after anaesthesia.
我们描述了一名患有弗里德赖希共济失调症的20岁女性患者行刮宫术时的麻醉管理情况。在使用噻吗洛尔、地西泮和阿托品进行术前用药后，用硫喷妥钠诱导麻醉。异氟烷和氧化亚氮用于维持麻醉。我们回顾了有关该疾病及其麻醉相关影响的文献。弗里德赖希共济失调症患者的麻醉风险包括潜在的心律失常和心力衰竭风险，以及对肌肉松弛剂的显著敏感性。呼吸并发症和糖尿病是术后的其他主要问题。我们得出结论，对于此类患者，在麻醉期间及之后应特别小心地进行监测，尤其是心血管功能和神经肌肉传递方面。
