Rac Goran, Ellet Justin D, Sarkissian Hagop, Eklund Meryle J, Stec Andrew A
Department of Urology, Medical University of South Carolina, Charleston, SC.
Department of Urology, Medical University of South Carolina, Charleston, SC.
Urology. 2016 Jul;93:188-90. doi: 10.1016/j.urology.2016.02.035. Epub 2016 Mar 3.
Wilms' tumor is the most common pediatric solid renal tumor. Cross-fused renal ectopia is a rare congenital anomaly in which the left and right kidneys become fused and fail to ascend from the pelvis and abdomen. We report a case of a 5-year-old girl that underwent open partial nephrectomy on a cross-fused ectopic kidney, "pancake kidney," after incidental discovery of a solid renal mass found to be a Wilms' tumor. Thorough review of the literature shows that this combination of Wilms' tumor in the setting of cross-fused renal ectopia has only been reported twice previously.
肾母细胞瘤是最常见的小儿实性肾肿瘤。交叉融合型肾异位是一种罕见的先天性异常,左右肾融合在一起,未能从盆腔和腹部上升。我们报告一例5岁女孩的病例,她在偶然发现一个实性肾肿块被诊断为肾母细胞瘤后,接受了对交叉融合异位肾(“饼状肾”)的开放性部分肾切除术。对文献的全面回顾显示,肾母细胞瘤合并交叉融合型肾异位的这种情况此前仅被报道过两次。