Kucharz E J, Sierakowski S J
Postepy Hig Med Dosw. 1989;43(1):93-102.
Scleroderma, a connective tissue disorder is characterized by vascular and interstitial reaction with deposition of matrix components. Abnormalities in collagen and glycosaminoglycan structure and metabolism, and regulatory processes of their biosynthesis in scleroderma are reviewed.
硬皮病是一种结缔组织疾病，其特征为血管和间质反应以及基质成分的沉积。本文综述了硬皮病中胶原蛋白和糖胺聚糖结构与代谢的异常，以及它们生物合成的调控过程。
