Huang Ying-Hsien, Kuo Ho-Chang, Huang Fu-Chen, Yu Hong-Ren, Hsieh Kai-Sheng, Yang Ya-Ling, Sheen Jiunn-Ming, Li Sung-Chou, Kuo Hsing-Chun
Department of Pediatrics, Kaohsiung Chang Gung Memorial Hospital and Chang Gung University College of Medicine, Kaohsiung 833, Taiwan.
Kawasaki Disease Center, Kaohsiung Chang Gung Memorial Hospital, Kaohsiung 833, Taiwan.
Int J Mol Sci. 2016 May 12;17(5):715. doi: 10.3390/ijms17050715.
Kawasaki disease (KD) is a type of systemic vasculitis that primarily affects children under the age of five years old. For sufferers of KD, intravenous immunoglobulin (IVIG) has been found to successfully diminish the occurrence of coronary artery lesions. Anemia is commonly found in KD patients, and we have shown that in appropriately elevated hepcidin levels are related to decreased hemoglobin levels in these patients. In this study, we investigated the time period of anemia and iron metabolism during different stages of KD. A total of 100 patients with KD and 20 control subjects were enrolled in this study for red blood cell and hemoglobin analysis. Furthermore, plasma, urine hepcidin, and plasma IL-6 levels were evaluated using enzyme-linked immunosorbent assay in 20 KD patients and controls. Changes in hemoglobin, plasma iron levels, and total iron binding capacity (TIBC) were also measured in patients with KD. Hemoglobin, iron levels, and TIBC were lower (p < 0.001, p = 0.009, and p < 0.001, respectively) while plasma IL-6 and hepcidin levels (both p < 0.001) were higher in patients with KD than in the controls prior to IVIG administration. Moreover, plasma hepcidin levels were positively and significantly correlated with urine hepcidin levels (p < 0.001) prior to IVIG administration. After IVIG treatment, plasma hepcidin and hemoglobin levels significantly decreased (both p < 0.001). Of particular note was a subsequent gradual increase in hemoglobin levels during the three weeks after IVIG treatment; nevertheless, the hemoglobin levels stayed lower in KD patients than in the controls (p = 0.045). These findings provide a longitudinal study of hemoglobin changes and among the first evidence that hepcidin induces transient anemia and hypoferremia during KD's acute inflammatory phase.
川崎病(KD)是一种主要影响五岁以下儿童的系统性血管炎。对于KD患者,已发现静脉注射免疫球蛋白(IVIG)可成功减少冠状动脉病变的发生。KD患者中常见贫血,并且我们已经表明,这些患者中适当升高的铁调素水平与血红蛋白水平降低有关。在本研究中,我们调查了KD不同阶段的贫血和铁代谢时期。本研究共纳入100例KD患者和20例对照受试者进行红细胞和血红蛋白分析。此外,使用酶联免疫吸附测定法评估了20例KD患者和对照受试者的血浆、尿铁调素和血浆IL-6水平。还测量了KD患者的血红蛋白、血浆铁水平和总铁结合力(TIBC)的变化。在IVIG给药前,KD患者的血红蛋白、铁水平和TIBC较低(分别为p < 0.001、p = 0.009和p < 0.001),而血浆IL-6和铁调素水平(均为p < 0.001)高于对照组。此外,在IVIG给药前,血浆铁调素水平与尿铁调素水平呈显著正相关(p < 0.001)。IVIG治疗后,血浆铁调素和血红蛋白水平显著降低(均为p < 0.001)。特别值得注意的是,IVIG治疗后的三周内血红蛋白水平随后逐渐升高;然而,KD患者的血红蛋白水平仍低于对照组(p = 0.045)。这些发现提供了关于血红蛋白变化的纵向研究,并且是铁调素在KD急性炎症期诱导短暂性贫血和低铁血症的首批证据之一。