Putzier M, Groß C, Zahn R K, Pumberger M, Strube P
Centrum für Muskuloskeletale Chirurgie, Klinik für Orthopädie, Charité - Universitätsmedizin Berlin, Charitéplatz 1, 10117, Berlin, Deutschland.
Klinik für Orthopädie und Unfallchirurgie, Helios Klinikum Emil von Behring, Walterhöferstraße 11, 14165, Berlin, Deutschland.
Orthopade. 2016 Jun;45(6):500-8. doi: 10.1007/s00132-016-3272-7.
Usually, neuromuscular scolioses become clinically symptomatic relatively early and are rapidly progressive even after the end of growth. Without sufficient treatment they lead to a severe reduction of quality of life, to a loss of the ability of walking, standing or sitting as well as to an impairment of the cardiopulmonary system resulting in an increased mortality. Therefore, an intensive interdisciplinary treatment by physio- and ergotherapists, internists, pediatricians, orthotists, and orthopedists is indispensable. In contrast to idiopathic scoliosis the treatment of patients with neuromuscular scoliosis with orthosis is controversially discussed, whereas physiotherapy is established and essential to prevent contractures and to maintain the residual sensorimotor function.Frequently, the surgical treatment of the scoliosis is indicated. It should be noted that only long-segment posterior correction and fusion of the whole deformity leads to a significant improvement of the quality of life as well as to a prevention of a progression of the scoliosis and the development of junctional problems. The surgical intervention is usually performed before the end of growth. A prolonged delay of surgical intervention does not result in an increased height but only in a deformity progression and is therefore not justifiable. In early onset neuromuscular scolioses guided-growth implants are used to guarantee the adequat development. Because of the high complication rates, further optimization of these implant systems with regard to efficiency and safety have to be addressed in future research.
通常,神经肌肉型脊柱侧凸在临床上相对较早出现症状,即使在生长结束后仍会迅速进展。如果没有足够的治疗,它们会导致生活质量严重下降,丧失行走、站立或坐立能力,以及损害心肺系统,从而增加死亡率。因此,物理治疗师、职业治疗师、内科医生、儿科医生、矫形师和骨科医生进行的强化多学科治疗是必不可少的。与特发性脊柱侧凸不同,对于神经肌肉型脊柱侧凸患者使用矫形器治疗存在争议,而物理治疗已确立且对于预防挛缩和维持残余感觉运动功能至关重要。脊柱侧凸的手术治疗常常是必要的。应当注意,只有对整个畸形进行长节段后路矫正和融合才能显著改善生活质量,并防止脊柱侧凸进展和出现交界性问题。手术干预通常在生长结束前进行。手术干预的长期延迟不会增加身高,只会导致畸形进展,因此是不合理的。在早发性神经肌肉型脊柱侧凸中,使用生长引导植入物来保证适当的发育。由于并发症发生率高,未来研究必须解决这些植入系统在效率和安全性方面的进一步优化问题。