Bairdain Sigrid, Zurakowski David, Baird Christopher W, Jennings Russell W
Department of Pediatric Surgery, Boston Children's Hospital, Boston, MA 02115.
Department of Pediatric Surgery, Boston Children's Hospital, Boston, MA 02115; Department of Anesthesia, Boston Children's Hospital, Boston MA 02115.
Paediatr Respir Rev. 2016 Jun;19:16-20. doi: 10.1016/j.prrv.2016.04.002. Epub 2016 Apr 28.
Tracheobronchomalacia, as a whole, is likely misdiagnosed and underestimated as a cause of respiratory compromise in pediatric patients. Currently, there is no standardized approach for the overall evaluation of pediatric tracheobronchomalacia (TBM) and the concept of excessive dynamic airway collapse (EDAC); no grading score for the evaluation of severity; nor a standardized means to successfully approach TBM and EDAC. This paper describes our experience standardizing the approach to these complex patients whose backgrounds include different disease etiologies, as well as a variety of comorbid conditions. Preoperative and postoperative evaluation of patients with severe TBM and EDAC, as well as concurrent development of a prospective grading scale, has allowed us to ascertain correlation between surgery, symptoms, and effectiveness on particular tracheal-bronchial segments. Long-term, continued collection of patient characteristics, surgical technique, complications, and outcomes must be collected given the overall heterogeneity of this particular population.
总体而言,气管支气管软化症作为小儿患者呼吸功能不全的一个病因,很可能被误诊和低估。目前,对于小儿气管支气管软化症(TBM)和过度动态气道塌陷(EDAC)的整体评估,尚无标准化方法;没有用于评估严重程度的分级评分;也没有成功处理TBM和EDAC的标准化手段。本文介绍了我们在使这些背景包括不同疾病病因以及多种合并症的复杂患者的处理方法标准化方面的经验。对重度TBM和EDAC患者进行术前和术后评估,并同时制定一个前瞻性分级量表,使我们能够确定手术、症状以及特定气管支气管节段的有效性之间的相关性。鉴于这一特定人群的总体异质性,必须长期持续收集患者特征、手术技术、并发症和预后情况。