Wagner M B, Vignos P J, Carlozzi C
Department of Medicine, University Hospitals of Cleveland, Ohio.
Muscle Nerve. 1989 Mar;12(3):236-44. doi: 10.1002/mus.880120313.
The wrist and hands of 18 Duchenne muscular dystrophy (DMD) patients were assessed for abnormalities. The subjects were divided into three groups by age. Flexion and ulnar deviation contractures of the wrist began in the youngest age group, 8-14 years. Other abnormalities, present in all age groups, included extrinsic and intrinsic digital muscle shortness, boutonniere and swan neck deformities, and hyperextension of the digital interphalangeal joints. Pain found with passive proximal interphalangeal joint flexion has not been reported previously. This study supports the importance of early assessment of the wrist and hand in DMD and suggests intervention techniques to possibly retard the deforming process.
对18名杜氏肌营养不良症(DMD)患者的手腕和手部进行了异常评估。根据年龄将受试者分为三组。手腕的屈曲和尺侧偏斜挛缩始于最年轻的年龄组,即8 - 14岁。所有年龄组都存在的其他异常包括外在和内在手指肌肉缩短、纽扣样和鹅颈样畸形以及手指指间关节的过度伸展。被动近端指间关节屈曲时出现的疼痛此前未见报道。本研究支持对DMD患者的手腕和手部进行早期评估的重要性,并提出了可能延缓变形过程的干预技术。