Burbelo Peter D, Iadarola Michael J, Alevizos Ilias, Sapio Matthew R
Dental Clinical Research Core, National Institute of Dental and Craniofacial Research, National Institutes of Health, Bldg. 10, Rm. 5N102, Bethesda, MD, 20892, USA.
Department of Perioperative Medicine, Clinical Center, National Institutes of Health, Bethesda, MD, USA.
Mol Diagn Ther. 2016 Oct;20(5):415-27. doi: 10.1007/s40291-016-0211-6.
The measurement of autoantibodies in the clinical care of autoimmune patients allows for diagnosis, monitoring, and even disease prediction. Despite their clinical utility, the functional significance of autoantibody target proteins in many autoimmune diseases remains unclear. Here we present a comprehensive review of 52 autoantigens commonly employed for the serological diagnosis of 24 autoimmune diseases. We discuss their function, whether they have extracellular-exposed epitopes, and whether antibodies to these proteins are known to be pathogenic. Transcriptomics (RNA-Seq) datasets were mined to display messenger RNA (mRNA) expression of the autoantigens across 32 tissues and organs. This analysis revealed that autoantigens cluster into one of three groups: expression in the tissue most strongly affected in the disease (Group I), ubiquitous expression with enrichment in immune tissues (Group II), or expression in other tissues not typically associated with the clinical presentation (Group III). Clustering demonstrated that the autoantigens within Group I were often proteins containing extracellular epitopes, many of which are targets of pathogenic autoantibodies. Group II autoantigens were targets for several rheumatological diseases, including Sjögren syndrome, systemic lupus erythematosus, myositis, and systemic sclerosis, and were ubiquitously expressed with enrichment in immune-rich tissues. This raises the possibility that immune cells in Group II disorders may be the source of autoimmunization and/or targets of immune cell responses. Since tissues showing enriched autoantigen gene expression may contribute to the development of autoantibodies and subsequent autoimmunity, the emergent patterns arising from the autoantigen transcriptomic profiles may provide a new heuristic framework to deconvolute these complex disorders.
在自身免疫性疾病的临床护理中,自身抗体的检测有助于诊断、监测甚至疾病预测。尽管它们具有临床实用性,但许多自身免疫性疾病中自身抗体靶蛋白的功能意义仍不清楚。在此,我们对常用于24种自身免疫性疾病血清学诊断的52种自身抗原进行了全面综述。我们讨论了它们的功能、是否具有细胞外暴露表位,以及针对这些蛋白的抗体是否已知具有致病性。我们挖掘了转录组学(RNA测序)数据集,以展示这些自身抗原在32个组织和器官中的信使核糖核酸(mRNA)表达。该分析揭示,自身抗原可分为三组之一:在疾病中受影响最严重的组织中表达(第一组)、在免疫组织中普遍表达且富集(第二组),或在通常与临床表现无关的其他组织中表达(第三组)。聚类分析表明,第一组中的自身抗原通常是含有细胞外表位的蛋白,其中许多是致病性自身抗体的靶标。第二组自身抗原是几种风湿性疾病的靶标,包括干燥综合征、系统性红斑狼疮、肌炎和系统性硬化症,并且在富含免疫细胞的组织中普遍表达且富集。这增加了第二组疾病中的免疫细胞可能是自身免疫的来源和/或免疫细胞反应靶标的可能性。由于显示自身抗原基因表达富集的组织可能有助于自身抗体的产生及随后的自身免疫,自身抗原转录组图谱中出现的模式可能为剖析这些复杂疾病提供一个新的启发式框架。