Aggarwal Sourabh, Kalavakunta Jagadeesh, Gupta Vishal
Department of Internal Medicine, Western Michigan University School of Medicine, Kalamazoo, Michigan.
Department of Cardiology, Borgess Heart Institute, Kalamazoo, Michigan.
Heart Views. 2016 Jan-Mar;17(1):30-4. doi: 10.4103/1995-705X.182645.
Non-compaction of ventricular myocardium (NCVM) is a rare genetic disorder caused by intrauterine arrest of endomyocardial development. Left ventricle is the usual site of NCVM with very rare reports of isolated right ventricular non-compaction (IRVNC). We describe a case of asymptomatic IRVNC with unique EKG changes.
心室心肌致密化不全(NCVM)是一种罕见的遗传性疾病,由心内膜发育的宫内停滞引起。左心室是NCVM的常见部位,孤立性右心室致密化不全(IRVNC)的报道非常罕见。我们描述了一例具有独特心电图改变的无症状IRVNC病例。