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1例孤立性右心室心肌致密化不全伴胸导联ST段抬高

A Case of Isolated Right Ventricle Noncompaction with ST-Elevation Chest Leads.

作者信息

Aggarwal Sourabh, Kalavakunta Jagadeesh, Gupta Vishal

机构信息

Department of Internal Medicine, Western Michigan University School of Medicine, Kalamazoo, Michigan.

Department of Cardiology, Borgess Heart Institute, Kalamazoo, Michigan.

出版信息

Heart Views. 2016 Jan-Mar;17(1):30-4. doi: 10.4103/1995-705X.182645.

DOI:10.4103/1995-705X.182645
PMID:27293528
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC4879803/
Abstract

Non-compaction of ventricular myocardium (NCVM) is a rare genetic disorder caused by intrauterine arrest of endomyocardial development. Left ventricle is the usual site of NCVM with very rare reports of isolated right ventricular non-compaction (IRVNC). We describe a case of asymptomatic IRVNC with unique EKG changes.

摘要

心室心肌致密化不全(NCVM)是一种罕见的遗传性疾病,由心内膜发育的宫内停滞引起。左心室是NCVM的常见部位,孤立性右心室致密化不全(IRVNC)的报道非常罕见。我们描述了一例具有独特心电图改变的无症状IRVNC病例。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/594d/4879803/0c05c12c6bbf/HV-17-30-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/594d/4879803/094b1dab3ace/HV-17-30-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/594d/4879803/06cee5758317/HV-17-30-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/594d/4879803/0c05c12c6bbf/HV-17-30-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/594d/4879803/094b1dab3ace/HV-17-30-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/594d/4879803/06cee5758317/HV-17-30-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/594d/4879803/0c05c12c6bbf/HV-17-30-g003.jpg

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Left ventricular noncompaction and myocardial fibrosis: a case report.左心室心肌致密化不全与心肌纤维化:一例报告
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