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An unusual case of isolated non-compacted right ventricular myocardium.

作者信息

Gomathi S Balashankar, Makadia Nilesh, Ajit S Mullasari

机构信息

Institute of Cardiovascular Diseases, Madras Medical Mission, 4-A, Dr J.J. Nagar, Mogappair, Chennai 600 037, Tamilnadu, India.

出版信息

Eur J Echocardiogr. 2008 May;9(3):424-5. doi: 10.1093/ejechocard/jen016. Epub 2008 Feb 12.

DOI:10.1093/ejechocard/jen016
PMID:18296401
Abstract

Isolated ventricular non-compaction is a rare type of cardiomyopathy resulting from arrested myocardial development during embryogenesis. This rare entity can be easily diagnosed by characteristic appearance of prominent myocardial trabeculations and deep inter-trabecular spaces. The clinical manifestations include heart failure signs, ventricular arrhythmias, and cardio-embolic events. Although the usual site of involvement is the left ventricle, the right ventricle (RV) can rarely be affected. Here, we report a case of 23-year-old male patient with isolated RV non-compaction.

摘要

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