Greenberg C R, Dilling L A, Thompson R, Ford J D, Seargeant L E, Haworth J C
University of Manitoba, Children's Hospital, Winnipeg, Canada.
Pediatrics. 1989 Aug;84(2):331-5.
In July 1983, the Manitoba Perinatal Screening Programme modified its existing procedure for neonatal screening for galactosemia by introducing quantitation of total galactose plus galactose-1-phosphate from dried blood spots using the Multistat centrifugal analyzer. The first 4 years of experience with this method in combination with the Beutler spot test for galactose-1-phosphate uridyl transferase activity is the subject of this report. Of 70,336 newborns screened, 142 (0.20%) met the criteria for clinical follow up. Of these, one child was confirmed to have classical galactosemia and nine children were found to be Duarte/galactosemia genetic compounds. This method of galactosemia screening has proven to be rapid, sensitive, efficient, and the method of choice for mass screening of disorders of galactose metabolism.
1983年7月,曼尼托巴围产期筛查项目修改了现有的新生儿半乳糖血症筛查程序,采用Multistat离心分析仪对干血斑中的总半乳糖和1-磷酸半乳糖进行定量检测。本报告的主题是该方法与用于检测1-磷酸半乳糖尿苷转移酶活性的Beutler斑点试验相结合的头4年经验。在70336名接受筛查的新生儿中,有142名(0.20%)符合临床随访标准。其中,一名儿童被确诊为典型半乳糖血症,九名儿童被发现是Duarte/半乳糖血症遗传复合物。这种半乳糖血症筛查方法已被证明是快速、灵敏、高效的,是大规模筛查半乳糖代谢紊乱的首选方法。