Kaselas Christos, Patoulias Dimitrios, Patoulias Ioannis, Spyridakis Ioannis
Pediatric Surgeon, 1 Department of Pediatric Surgery, "G. Gennimatas" University Hospital, "Aristotle" University of Thessaloniki , Thessaloniki, Greece .
Medical Student, 1 Department of Pediatric Surgery, "G. Gennimatas" University Hospital, "Aristotle" University of Thessaloniki , Thessaloniki, Greece .
J Clin Diagn Res. 2016 Jun;10(6):PD07-9. doi: 10.7860/JCDR/2016/20630.8000. Epub 2016 Jun 1.
Choledochal cysts are rare congenital malformations, comprising of dilatation of the biliary tree of different localization. Classically, classification of choledochal cysts describes five variants of the disease. Type VI choledochal cyst is considered by many authors as the sixth variant of this classification and is described either as a dilatation of the cystic duct or as a cystic duct cyst. We present a rare case of cystic duct dilatation that presented with acute cholangiopancreatitis and a clinical picture consistent of a choledochal cyst in a 10-year-old female patient. Cholecystectomy with excision of the cystic duct was performed. Histopathologic examination did not reveal any findings consistent with choledochal cyst. Based on these findings we speculate that in our case the dilatation of the cystic duct is a variant to type VI choledochal cyst, based on the fact that no cystic-like malformation has been identified in histology. We provide details of the pre-operative work-up and compare them with intraoperative findings in order to increase awareness of the condition.
胆管囊肿是一种罕见的先天性畸形，由不同部位的胆管树扩张组成。传统上，胆管囊肿的分类描述了该疾病的五种变体。许多作者认为Ⅵ型胆管囊肿是这种分类的第六种变体，被描述为胆囊管扩张或胆囊管囊肿。我们报告了一例罕见的胆囊管扩张病例，该病例表现为急性胆胰炎，临床症状与一名10岁女性患者的胆管囊肿一致。实施了胆囊切除术并切除了胆囊管。组织病理学检查未发现任何与胆管囊肿相符的结果。基于这些发现，我们推测在我们的病例中，胆囊管扩张是Ⅵ型胆管囊肿的一种变体，因为在组织学上未发现囊性畸形。我们提供术前检查的详细信息，并将其与术中发现进行比较，以提高对该病症的认识。
