Al Umairi Rashid Saif, Al Kindi Faiza, Al Busaidi Fadhila
Oman Medical Specialty Board, Muscat, Oman; Royal Hospital, Muscat, Oman.
Oman Medical Specialty Board, Muscat, Oman.
Oman Med J. 2016 Sep;31(5):387-9. doi: 10.5001/omj.2016.77.
Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is a rare congenital coronary abnormality also known as Bland-White-Garland syndrome. The incidence of ALCAPA is about 1 in every 300,000 live births, and constitutes 0.24% and 0.46% of all congenital cardiac disease. It has a high infant mortality rate reaching up to 90% if left untreated. For many years, the diagnosis of ALCAPA was by angiography or autopsy. However, multislice computed tomography (MSCT) is a non-invasive imaging tool that allows accurate, non-invasive diagnosis of ALCAPA. Here we report a case of ALCAPA in a six-month-old girl who presented with a two-week history of cough, fever, tachypnea, and sweating during feeding. During admission, an echocardiogram was performed that revealed ALCAPA, which was confirmed using CT. We discuss the role of MSCT in its diagnosis.
左冠状动脉起源于肺动脉（ALCAPA）是一种罕见的先天性冠状动脉异常，也被称为布兰德 - 怀特 - 加兰综合征。ALCAPA的发病率约为每30万活产中有1例，占所有先天性心脏病的0.24%和0.46%。如果不进行治疗，其婴儿死亡率很高，可达90%。多年来，ALCAPA的诊断依靠血管造影或尸检。然而，多层螺旋计算机断层扫描（MSCT）是一种非侵入性成像工具，能够对ALCAPA进行准确的非侵入性诊断。在此，我们报告一例6个月大女童的ALCAPA病例，该女童有两周的咳嗽、发热、呼吸急促及喂奶时出汗的病史。入院期间进行了超声心动图检查，结果显示为ALCAPA，随后通过CT得以确诊。我们讨论了MSCT在其诊断中的作用。
