Wang Haitao, Fang Fang, Sun Ying, Wang Songlan, Mao Yonghui
Department of Nephrolgy Department of Pathology, Beijing Hospital, National Center of Gerontology, China.
Medicine (Baltimore). 2016 Oct;95(41):e5086. doi: 10.1097/MD.0000000000005086.
Kimura disease is a rare chronic inflammatory disorder with peripheral eosinophilia and elevated serum IgE and is also frequently complicated by nephropathy.
We report a rare case of Kimura disease concomitant with lupus nephritis in a 72-year old male patient with recurrent unexplained lymphadenopathy, renal lesions, and immunologic abnormalities.
The patient was successfully managed with gamma immunoglobulin, intravenous pulse methylprednisolone therapy, hydroxychloroquine, and prednisone.
This is the first report of a case of Kimura disease concomitant with lupus nephritis and highlights the importance of considering lupus nephritis as a possible concurrent disease in patients with Kimura disease that have immunologic abnormalities.
木村病是一种罕见的慢性炎症性疾病，伴有外周嗜酸性粒细胞增多和血清IgE升高，且常并发肾病。
我们报告了一例罕见的木村病合并狼疮性肾炎的病例，患者为一名72岁男性，反复出现不明原因的淋巴结病、肾脏病变和免疫异常。
该患者通过γ免疫球蛋白、静脉注射脉冲甲基强的松龙治疗、羟氯喹和强的松成功得到治疗。
这是首例木村病合并狼疮性肾炎的病例报告，强调了在患有免疫异常的木村病患者中，将狼疮性肾炎视为可能的并发疾病的重要性。
