Kim Il-Kyu, Cho Hyun-Young, Jung Bum-Sang, Pae Sang-Pill, Cho Hyun-Woo, Seo Ji-Hoon, Park Seung-Hoon
Division of Oral and Maxillofacial Surgery, Department of Dentistry, Inha University School of Medicine, Incheon, Korea.
Department of Oral and Maxillofacial Surgery, Catholic Kwandong University International St. Mary's Hospital, Incheon, Korea.
J Korean Assoc Oral Maxillofac Surg. 2016 Oct;42(5):307-314. doi: 10.5125/jkaoms.2016.42.5.307. Epub 2016 Oct 25.
We report a case of retiform hemangioendothelioma (RH) located in the infratemporal fossa and buccal area in a 13-year-old Korean boy. The tumor originated from the sphenoid bone of the infratemporal fossa area and spread into the cavernous sinus, orbital apex, and retro-nasal area with bone destruction of the pterygoid process. Tumor resection was conducted via Le Fort I osteotomy and partial maxillectomy to approach the infratemporal fossa and retro-nasal area. The diagnosis of RH was confirmed after surgery. In the presented patient, surgical excision was incomplete, and close follow-up was performed. There was no evidence of expansion or metastasis of the residual tumor in the 8 years after surgery. In cases of residual RH with low likelihood of expansion and metastasis, even though RH is an intermediate malignancy, close follow-up can be the appropriate treatment choice over additional aggressive therapy. To date, 29 papers and 48 RH cases have been reported, including this case. This case is the second reported RH case presenting as primary bone tumor and the first case originating in the oromaxillofacial area.
我们报告了一例位于一名13岁韩国男孩颞下窝和颊部区域的网状血管内皮瘤（RH）。肿瘤起源于颞下窝区域的蝶骨，并蔓延至海绵窦、眶尖和鼻后区域，翼突骨质破坏。通过Le Fort I截骨术和部分上颌骨切除术进行肿瘤切除，以接近颞下窝和鼻后区域。术后确诊为RH。在本病例中，手术切除不完全，因此进行了密切随访。术后8年没有残余肿瘤扩大或转移的证据。对于残余RH且扩大和转移可能性低的病例，尽管RH是一种中度恶性肿瘤，但密切随访可能是比额外积极治疗更合适的治疗选择。迄今为止，包括本病例在内，已报告了29篇论文和48例RH病例。本病例是第二例报告的以原发性骨肿瘤形式出现的RH病例，也是第一例起源于口腔颌面区域的病例。
