Tomar Than Singh, Sambasivan Suchetha, Nair Rema Prabhakaran, Thomas Shaji, Ramadas Preethi T
Regional Cancer Centre (RCC), Medical College Campus, Trivandrum, Kerala 695011 India.
Indian J Surg Oncol. 2016 Dec;7(4):488-490. doi: 10.1007/s13193-016-0551-z. Epub 2016 Aug 25.
Extra mammary Paget's disease (EMPD) is a rare condition involving the vulva, anogenital region, and axilla. Vulvar disease usually presents as a slow growing well-defined itchy plaque with crustations or ulcerations over the affected area in postmenopausal women. Well-established guidelines for diagnosis and management are not available for this rare condition. Our patient is a 64-year-old postmenopausal woman with a history of similar complaints of 2 years duration, not responding to multiple topical treatments. She was diagnosed with EMPD on incisional biopsy and treated with surgery at our centre.
乳腺外佩吉特病(EMPD)是一种罕见的疾病,累及外阴、肛门生殖器区域和腋窝。外阴疾病通常表现为绝经后女性受影响区域出现生长缓慢、边界清晰的瘙痒性斑块,伴有结痂或溃疡。对于这种罕见疾病,目前尚无成熟的诊断和治疗指南。我们的患者是一位64岁的绝经后女性,有长达2年的类似症状病史,对多种局部治疗均无反应。她在切开活检后被诊断为EMPD,并在我们中心接受了手术治疗。