Noel Alvish, Bhat Ramesh M, Rao Sujaya V, Fernandes Shannon
Department of Dermatology and, Father Muller Medical College Hospital, Mangalore, Karnataka, India.
Department of OBG, Father Muller Medical College Hospital, Mangalore, Karnataka, India.
Indian J Sex Transm Dis AIDS. 2020 Jul-Dec;41(2):210-212. doi: 10.4103/ijstd.IJSTD_69_19. Epub 2020 Nov 11.
Extramammary Paget's disease (EMPD) of the vulva is a rare disease that occurs mainly in postmenopausal women. It can be primary or secondary. Prognosis of primary EMPD is good, but when secondary, we need to find the underlying malignancy as the prognosis depends on it. Very few cases of secondary EMPD of the vulva have been reported till now. We hereby report a case of a 65-year-old postmenopausal woman with EMPD secondary to invasive adenocarcinoma with neuroendocrine features in the dermis and she was treated surgically followed by radiotherapy.
外阴部乳腺外佩吉特病（EMPD）是一种罕见疾病，主要发生在绝经后女性。它可以是原发性的，也可以是继发性的。原发性EMPD的预后良好，但若是继发性的，我们需要找出潜在的恶性肿瘤，因为预后取决于此。到目前为止，外阴继发性EMPD的病例报道非常少。我们在此报告一例65岁绝经后女性，其外阴EMPD继发于真皮层具有神经内分泌特征的浸润性腺癌，她接受了手术治疗，随后进行了放疗。
