Onubogu Uchenna, West Boma, Orupabo-Oyan Boma
Braithwaite Memorial Specialist Hospital, Portharcourt, Rivers, Nigeria.
Braithwaite Memorial Specialist Hospital, Portharcourt, Rivers, Nigeria. Email:
Cardiovasc J Afr. 2017;28(5):e1-e3. doi: 10.5830/CVJA-2016-093. Epub 2016 Dec 12.
Atrial myxoma is an uncommon cause of hemiplegia in children. However hemiplegia is the commonest manifestation of atrial myxoma in the paediatric age group.
An 11-year-old girl presented with left hemiplegia and palpitations. Three months later she had a deepvein thrombosis of the right common iliac vein. MRI of the brain showed a subacute right thalamic infarct, and an ECG showed left atrial and left ventricular hypertrophy. Transthoracic echocardiography revealed a left atrial myxoma impinging on the mitral valve. A diagnosis of left atrial myxoma with multiple thromboembolic events was made. She was placed on anticoagulants until she died while awaiting surgical tumour resection.
Echocardiography should be done early in children presenting with ischaemic thromboembolic diseases in order to reduce morbidity and mortality rates resulting from cardiac pathology.
心房黏液瘤是儿童偏瘫的罕见病因。然而,偏瘫是儿童年龄组中心房黏液瘤最常见的表现。
一名11岁女孩出现左偏瘫和心悸。三个月后,她出现右髂总静脉深静脉血栓形成。脑部MRI显示亚急性右丘脑梗死,心电图显示左心房和左心室肥大。经胸超声心动图显示左心房黏液瘤压迫二尖瓣。诊断为左心房黏液瘤伴多发血栓栓塞事件。在等待手术切除肿瘤期间,她一直服用抗凝剂,直至死亡。
对于出现缺血性血栓栓塞疾病的儿童,应尽早进行超声心动图检查,以降低心脏病变导致的发病率和死亡率。