Adams Scott J, Wong Melody, Haji Tahereh, Sohail Shahmir, Almubarak Salah
College of Medicine, University of Saskatchewan, Saskatoon, SK, Canada.
Division of Pediatric Neurology, Department of Pediatrics, University of Saskatchewan, Saskatoon, SK, Canada.
Case Rep Neurol Med. 2016;2016:9238310. doi: 10.1155/2016/9238310. Epub 2016 Nov 16.
Absence status epilepticus is characterized by a prolonged state of impaired consciousness or altered sensorium with generalized electroencephalographic abnormalities. It is most commonly diagnosed in patients with known idiopathic generalized epilepsy; however, it may also be the first presentation of epilepsy. Due to the subtle and variable manifestations of the condition, absence status epilepticus may be underrecognized, particularly in children. We present the case of an 8-year-old boy who experienced two episodes of prolonged altered mental status, subsequently determined to be absence status epilepticus with idiopathic generalized epilepsy with phantom absences. We discuss the classification, pathophysiology, clinical presentation, and electroencephalographic findings of pediatric absence status epilepticus and provide a practical overview for management.
失神癫痫持续状态的特征是意识受损或感觉改变的延长状态，并伴有广泛性脑电图异常。它最常见于已知特发性全身性癫痫的患者；然而，它也可能是癫痫的首次表现。由于该病症的表现微妙且多变，失神癫痫持续状态可能未得到充分认识，尤其是在儿童中。我们报告了一名8岁男孩的病例，他经历了两次精神状态改变延长的发作，随后被确定为伴有幻影失神的特发性全身性癫痫的失神癫痫持续状态。我们讨论了小儿失神癫痫持续状态的分类、病理生理学、临床表现和脑电图结果，并提供了实用的管理概述。
