Berhili Soufiane, Aissa Abdellah, Kadiri Selma, Cherradi Nadia, El Majjaoui Sanae, El Kacemi Hanan, Kebdani Tayeb, Benjaafar Noureddine
1 Radiotherapy Department, National Oncology Institute, Mohamed V University in Rabat, Morocco.
2 Cytopathology Laboratory, Ibn Sina Specialty Hospital, Mohamed V University in Rabat, Morocco.
Neuroradiol J. 2017 Jun;30(3):281-285. doi: 10.1177/1971400916687584. Epub 2017 Jan 6.
Background Ependymomas are rare adult tumors that originate from the ventricular system or the ependymal surface of the central canal. Extra-axial supratentorial ependymomas are extremely rare, and only five cases have been reported to date in the English literature. Case presentation A 46-year-old previously healthy male presented with a gradual painless loss of vision in the right eye. Cerebral MRI showed a right parietal-occipital lesion resembling an atypical meningioma. Surgical resection was performed, and immunohistochemical staining results concluded that it was a very uncommon location of a grade 3 ependymoma. Favorable outcome was observed one year after completion of postoperative radiotherapy. Conclusion Clinical and imaging aspects are misleading in rare brain tumors, and immunohistochemistry is essential to re-address diagnosis.
室管膜瘤是起源于脑室系统或中央管室管膜表面的罕见成人肿瘤。轴外幕上室管膜瘤极为罕见，迄今为止英文文献中仅报道过5例。病例报告：一名46岁既往健康男性出现右眼逐渐无痛性视力丧失。脑部MRI显示右顶枕叶病变，类似非典型脑膜瘤。进行了手术切除，免疫组化染色结果显示这是一例3级室管膜瘤的非常罕见的部位。术后放疗结束一年后观察到良好的结果。结论：在罕见脑肿瘤中，临床和影像学表现具有误导性，免疫组化对于重新明确诊断至关重要。
