Donich D, Lee J H, Prayson R
Department of Neurological Surgery, The Cleveland Clinic Foundation, Ohio 44195, USA.
Neurosurgery. 1999 Jan;44(1):195-8. doi: 10.1097/00006123-199901000-00116.
The presentation, diagnosis, and treatment are described for a patient with a giant ependymoma involving the right cerebellopontine angle extending into the cavernous sinus. This case presents the unusual occurrence of a large extra-axial intracranial ependymoma and is the first reported case of cavernous sinus extension of this tumor.
The patient was a 22-year-old woman who presented with a 3-day history of generalized headache and right-sided facial droop. Magnetic resonance imaging revealed a nonhomogeneously enhancing cystic mass that was primarily in the posterior fossa with significant supratentorial extension and no apparent intra-axial or intraventricular involvement.
Gross total resection of this mass was achieved via two-staged resections using an initial presigmoid transpetrous, transtentorial approach and a subsequent pterional craniotomy. Pathological evaluation confirmed the diagnosis of ependymoma, and adjuvant radiation therapy to the resection bed was administered.
Ependymomas can present as entirely extra-axial intracranial masses and rarely may involve the confines of the cavernous sinus.
描述了一名患有巨大室管膜瘤的患者的临床表现、诊断及治疗情况,该肿瘤累及右侧桥小脑角并延伸至海绵窦。此病例呈现出罕见的大型轴外颅内室管膜瘤,且是该肿瘤海绵窦延伸的首例报道病例。
患者为一名22岁女性,有3天的全身性头痛及右侧面部下垂病史。磁共振成像显示一个不均匀强化的囊性肿块,主要位于后颅窝,有明显的幕上延伸,且无明显的轴内或脑室内受累。
通过分两阶段切除实现了该肿块的全切除,最初采用乙状窦前经岩骨、经小脑幕入路,随后进行翼点开颅术。病理评估确诊为室管膜瘤,并对切除床进行了辅助放疗。
室管膜瘤可表现为完全位于轴外的颅内肿块,且很少累及海绵窦范围。