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腹腔镜治疗正中弓状韧带综合征:慢性严重腹痛的罕见病因

Laparoscopic Treatment of Median Arcuate Ligament Syndrome: A Rare Cause of Chronic Severe Abdominal Pain.

作者信息

Divarci Emre, Celtik Ulgen, Dokumcu Zafer, Celik Ahmet, Ergun Orkan

机构信息

Department of Pediatric Surgery, Faculty of Medicine, Ege University, İzmir, Turkey.

出版信息

J Indian Assoc Pediatr Surg. 2017 Jan-Mar;22(1):48-50. doi: 10.4103/0971-9261.194624.

DOI:10.4103/0971-9261.194624
PMID:28082779
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5217142/
Abstract

Median arcuate ligament syndrome is a rare disorder characterized by chronic postprandial abdominal pain and weight loss caused by compression on celiac artery. A 17-year-old girl with chronic severe abdominal pain and weight loss was referred to our clinic. Other causes of chronic abdominal pain were investigated and excluded. The compression on celiac artery was detected on Doppler ultrasound and diagnosis was confirmed by computed tomography angiography. The patient underwent laparoscopic release of median arcuate ligament. There were no intraoperative complications; however, partial pain response was observed postoperatively that necessitated para-spinal ganglion blockage. The patient is symptom-free in 1-year follow-up period.

摘要

正中弓状韧带综合征是一种罕见的疾病,其特征为餐后慢性腹痛和体重减轻,由腹腔干受压所致。一名17岁慢性严重腹痛和体重减轻的女孩被转诊至我院门诊。对慢性腹痛的其他病因进行了调查并排除。通过多普勒超声检测到腹腔干受压,并经计算机断层血管造影证实诊断。患者接受了腹腔镜下正中弓状韧带松解术。术中无并发症;然而,术后观察到部分疼痛缓解,需要进行椎旁神经节阻滞。在1年的随访期内,患者无症状。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a7f6/5217142/750a33dd0542/JIAPS-22-48-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a7f6/5217142/6088674e4e67/JIAPS-22-48-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a7f6/5217142/750a33dd0542/JIAPS-22-48-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a7f6/5217142/6088674e4e67/JIAPS-22-48-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/a7f6/5217142/750a33dd0542/JIAPS-22-48-g002.jpg

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本文引用的文献

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Pediatric median arcuate ligament syndrome: surgical outcomes and quality of life.小儿正中弓状韧带综合征:手术效果与生活质量
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Median arcuate ligament syndrome in the pediatric population.儿童人群中的正中弓状韧带综合征。
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