Scrimgeour Laura A, Grada Zakaria, Aswad Bassam I, Ng Thomas
Department of Surgery, Warren Alpert Medical School of Brown University, Providence, Rhode Island.
Department of Pathology, Warren Alpert Medical School of Brown University, Providence, Rhode Island.
Ann Thorac Surg. 2017 Feb;103(2):e135-e137. doi: 10.1016/j.athoracsur.2016.07.006.
We describe a patient with Doege-Potter syndrome (solitary fibrous tumor of the pleura presenting with hypoglycemia) and illustrate several important lessons learned from the case. Seven years after the initial diagnosis, the tumor showed significant growth and developed a high-grade undifferentiated component. Solitary fibrous tumors do grow and cannot be deemed benign. Resection should be considered in all patients who are candidates for operation upon diagnosis. Our case also serves as a reminder of this rare syndrome, inasmuch as early recognition of the association of hypoglycemia with these tumors may have allowed for earlier diagnosis and avoidance of extensive tests in our patient.
我们描述了一名患有多伊奇-波特综合征（伴有低血糖的胸膜孤立性纤维瘤）的患者，并阐述了从该病例中学到的几个重要经验教训。初次诊断七年后，肿瘤显著生长并出现了高级别未分化成分。孤立性纤维瘤确实会生长，不能被视为良性。对于所有诊断后适合手术的患者，都应考虑进行切除。我们的病例也提醒人们注意这种罕见综合征，因为早期认识到低血糖与这些肿瘤的关联，可能会使我们的患者得到更早的诊断并避免进行大量检查。
