Kim Do Wan, Na Kook Joo, Yun Ju Sik, Song Sang Yun
Department of Thoracic and Cardiovascular Surgery, Chonnam National University Hwasun Hospital, Chonnam National University Medical School, 322 Seoyang-ro, Hwasun, 519-763, Korea.
J Cardiothorac Surg. 2017 Aug 7;12(1):64. doi: 10.1186/s13019-017-0630-4.
Solitary fibrous tumors of the pleura (SFTPs) are relatively rare tumors that originate from mesenchymal cells of submesothelial tissue of the pleura. Most patients with SFTPs are asymptomatic; however, pleuritic chest pain, cough, and dyspnea can develop. If hypoglycemia is associated with a solitary fibrous tumor, it is referred to as the Doege-Potter syndrome.
A 70-year-old man had visited our hospital with a chief complaint of dyspnea, and he was diagnosed as having a solitary fibrous tumor. A few years later, he developed hypoglycemia, and he underwent excision of the mass.
Occasionally, SFTPs induce several paraneoplastic events, such as hypertrophic osteoarthropathy. We described here a patient with an SFTP with Doege-Potter syndrome who was successfully treated with complete resection. Although lesions can be histologically benign, they can clinically present with malignant features.
胸膜孤立性纤维瘤（SFTPs）是相对罕见的肿瘤，起源于胸膜间皮下组织的间充质细胞。大多数SFTPs患者无症状；然而，可出现胸膜炎性胸痛、咳嗽和呼吸困难。如果低血糖与孤立性纤维瘤相关，则称为多伊格-波特综合征。
一名70岁男性因呼吸困难为主诉前来我院就诊，被诊断为患有孤立性纤维瘤。几年后，他出现低血糖，并接受了肿块切除术。
偶尔，SFTPs会引发几种副肿瘤性事件，如肥大性骨关节病。我们在此描述了一名患有多伊格-波特综合征的SFTP患者，通过完全切除成功治愈。尽管病变在组织学上可能是良性的，但在临床上可能表现出恶性特征。
