多伊格-波特综合征：一例组织学上为良性但临床上为恶性病例的报告。
Doege-potter syndrome: a report of a histologically benign but clinically malignant case.
作者信息
Kim Do Wan, Na Kook Joo, Yun Ju Sik, Song Sang Yun
机构信息
Department of Thoracic and Cardiovascular Surgery, Chonnam National University Hwasun Hospital, Chonnam National University Medical School, 322 Seoyang-ro, Hwasun, 519-763, Korea.
出版信息
J Cardiothorac Surg. 2017 Aug 7;12(1):64. doi: 10.1186/s13019-017-0630-4.
BACKGROUND
Solitary fibrous tumors of the pleura (SFTPs) are relatively rare tumors that originate from mesenchymal cells of submesothelial tissue of the pleura. Most patients with SFTPs are asymptomatic; however, pleuritic chest pain, cough, and dyspnea can develop. If hypoglycemia is associated with a solitary fibrous tumor, it is referred to as the Doege-Potter syndrome.
CASE PRESENTATION
A 70-year-old man had visited our hospital with a chief complaint of dyspnea, and he was diagnosed as having a solitary fibrous tumor. A few years later, he developed hypoglycemia, and he underwent excision of the mass.
CONCLUSION
Occasionally, SFTPs induce several paraneoplastic events, such as hypertrophic osteoarthropathy. We described here a patient with an SFTP with Doege-Potter syndrome who was successfully treated with complete resection. Although lesions can be histologically benign, they can clinically present with malignant features.
背景
胸膜孤立性纤维瘤（SFTPs）是相对罕见的肿瘤，起源于胸膜间皮下组织的间充质细胞。大多数SFTPs患者无症状；然而，可出现胸膜炎性胸痛、咳嗽和呼吸困难。如果低血糖与孤立性纤维瘤相关，则称为多伊格-波特综合征。
病例介绍
一名70岁男性因呼吸困难为主诉前来我院就诊，被诊断为患有孤立性纤维瘤。几年后，他出现低血糖，并接受了肿块切除术。
结论
偶尔，SFTPs会引发几种副肿瘤性事件，如肥大性骨关节病。我们在此描述了一名患有多伊格-波特综合征的SFTP患者，通过完全切除成功治愈。尽管病变在组织学上可能是良性的，但在临床上可能表现出恶性特征。
Zotero 插件