Dishner W, Cordasco E M, Blackburn J, Demeter S, Levin H, Carey W D
Chest. 1984 Jun;85(6):796-9. doi: 10.1378/chest.85.6.796.
Lymphangiomyomatosis is an interesting disease with distinctive clinical and histopathologic findings. We report herein two additional cases of lymphangiomyomatosis, including one with clinical improvement after therapy with progesterone. This case is of particular significance in view of the patient's negative sex steroid receptor analysis. These findings open new avenues for future considerations in the therapy of this unusual but interesting disease.
淋巴管平滑肌瘤病是一种具有独特临床和组织病理学表现的有趣疾病。我们在此报告另外两例淋巴管平滑肌瘤病病例，其中一例经孕酮治疗后临床症状改善。鉴于该患者性类固醇受体分析结果为阴性，此病例具有特殊意义。这些发现为治疗这种罕见但有趣的疾病开辟了新的思路。
