Mukherjee Bipasha, Alam Md Shahid
Department of Orbit Oculoplasty Reconstructive and Aesthetic Services, Sankara Nethralaya, Medical Research Foundation, Chennai, Tamil Nadu, India.
Indian J Ophthalmol. 2016 Dec;64(12):938-940. doi: 10.4103/0301-4738.198865.
Pachydermoperiostosis (PDP) is a multisystem disorder of mesenchymal origin. It is a form of hypertrophic osteoarthropathy. The typical clinical features include pachydermia, cutis verticus gyrata, digital clubbing, and periostosis. Patients present with mechanical ptosis resulting from markedly thickened eye lids. Floppy eye lids have rarely been reported in association with PDP. We describe a rare case of PDP associated with ptosis and floppy eye lids in an adult male. Meibomian gland dysfunction was documented by meibography. The patient underwent bilateral upper lid wedge resection, lateral tarsal strip, tarsectomy and external levator advancement with good cosmetic outcome following surgery.
厚皮性骨膜病（PDP）是一种间充质起源的多系统疾病。它是肥厚性骨关节病的一种形式。典型的临床特征包括厚皮症、回旋状头皮、杵状指和骨膜增生。患者因眼睑明显增厚而出现机械性上睑下垂。与PDP相关的松弛性眼睑鲜有报道。我们描述了一名成年男性罕见的PDP病例，该病例伴有上睑下垂和松弛性眼睑。睑板腺造影记录了睑板腺功能障碍。患者接受了双侧上睑楔形切除术、外侧睑板条手术、睑板切除术和外直肌缩短术，术后美容效果良好。
