Tripathy Koushik, Chawla Rohan, Mittal Kanhaiya, Farmania Rajni, Venkatesh Pradeep, Gulati Sheffali
Department of Retina and Uvea, Dr. Rajendra Prasad Centre for Ophthalmic Sciences, All India Institute of Medical Sciences (AIIMS), New Delhi, 110029 India.
Department of Pediatric Neurology, All India Institute of Medical Sciences (AIIMS), New Delhi, 110029 India.
Eye Vis (Lond). 2017 Jan 19;4:1. doi: 10.1186/s40662-016-0066-2. eCollection 2017.
Subacute sclerosing panencephalitis (SSPE) is a potentially fatal complication of measles. The authors report a case of recurrent myoclonic jerks under investigation, whose ophthalmic examination pointed to the diagnosis.
A 12-year-old boy with recurrent episodes of myoclonic jerks was found to have optic disc pallor and an irregular macular scar with pigmentation in the left eye. The retinal finding proved to be a strong diagnostic clue for SSPE. There was a history of exanthematous fever in childhood. Antibodies against measles were detected in both the cerebrospinal fluid and serum. Retinitis with intraretinal and subretinal hemorrhage in the right eye was noted 6-weeks after the initial presentation.
The authors describe the importance of ophthalmic evaluation in cases of recurrent myoclonic jerks. Optical coherence tomographic features and ultrawide field imaging characteristics of a case of SSPE are described.
亚急性硬化性全脑炎（SSPE）是麻疹的一种潜在致命并发症。作者报告了一例正在接受调查的反复肌阵挛性抽搐病例，其眼科检查指向了该诊断。
一名12岁反复出现肌阵挛性抽搐发作的男孩，被发现左眼视盘苍白，黄斑区有不规则瘢痕并伴有色素沉着。视网膜检查结果被证明是SSPE的一个有力诊断线索。该男孩有儿童期出疹性发热病史。脑脊液和血清中均检测到抗麻疹抗体。初次就诊6周后，右眼出现视网膜内和视网膜下出血的视网膜炎。
作者描述了眼科评估在反复肌阵挛性抽搐病例中的重要性。描述了一例SSPE的光学相干断层扫描特征和超广角成像特征。
