Hajjar Joud, Guffey Danielle, Minard Charles G, Orange Jordan S
Section of Immunology, Allergy and Rheumatology, Department of Pediatrics, Baylor College of Medicine, Houston, TX, USA.
Texas Children's Hospital, Houston, TX, USA.
J Clin Immunol. 2017 Feb;37(2):153-165. doi: 10.1007/s10875-016-0367-1. Epub 2017 Jan 26.
Patients with primary immunodeficiency (PID) often report fatigue, yet this symptom has not been studied in PID. Fatigue affects 6-7.5% of healthy adults. The goal of this study is to estimate the prevalence of fatigue in patients with PID and investigate its associated factors.
We analyzed 2537 PID patients registered in USIDNET to determine responses to the field "fatigue" in the core registry form. Demographics, immune phenotypes, and comorbid conditions were compared between fatigued and non-fatigued patients to identify relevant associations and potential drivers. A focused analysis was performed for patients with predominantly antibody deficiency disorders (PADs).
Fatigue was reported in 25.9% (95% CI 23.7-28.3) of PAD patients, compared to 6.4% (95% CI 4.9-8.2) of non-PAD. Patients with common variable immunodeficiency (CVID) had the highest prevalence of fatigue (p < 0.001) among all PID diagnoses. Other factors that were associated with a higher rate of fatigue among PAD patients included female sex, higher BMI, depression, bronchiectasis, and autoimmunity. Additionally, fatigued PAD patients had lower absolute lymphocyte, CD3, CD4, and CD8 counts compared to non-fatigued patients.
Our findings suggest that fatigue is overrepresented in PAD patients. Prospective studies to estimate prevalence, risk factors, and fatigue etiology in PID are warranted, so therapeutic interventions can be considered.
原发性免疫缺陷(PID)患者常报告有疲劳症状,但该症状在PID中尚未得到研究。疲劳影响6 - 7.5%的健康成年人。本研究的目的是估计PID患者中疲劳的患病率,并调查其相关因素。
我们分析了在美国免疫缺陷网络(USIDNET)注册的2537例PID患者,以确定核心注册表中“疲劳”字段的回答情况。比较了疲劳患者和非疲劳患者的人口统计学、免疫表型和合并症,以确定相关关联和潜在驱动因素。对主要为抗体缺陷疾病(PAD)的患者进行了重点分析。
PAD患者中有25.9%(95%置信区间23.7 - 28.3)报告有疲劳,而非PAD患者为6.4%(95%置信区间4.9 - 8.2)。在所有PID诊断中,常见变异型免疫缺陷(CVID)患者的疲劳患病率最高(p < 0.001)。PAD患者中与较高疲劳率相关的其他因素包括女性、较高的体重指数、抑郁、支气管扩张和自身免疫。此外,与非疲劳的PAD患者相比,疲劳的PAD患者的绝对淋巴细胞、CD3、CD4和CD8计数较低。
我们的研究结果表明,PAD患者中疲劳的比例过高。有必要进行前瞻性研究以估计PID中疲劳的患病率、危险因素和病因,以便考虑治疗干预措施。