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水通道蛋白4抗体阳性视神经脊髓炎谱系障碍一例的磁共振成像脑部表现,伴有顽固性呕吐和呃逆。

Magnetic resonance imaging brain findings in a case of aquaporin-4 antibody-positive neuromyelitis optica spectrum disorder, presenting with intractable vomiting and hiccups.

作者信息

Garg Prerna, Rajasekaran Muthusubramanian, Pandey Salil, Gurusamy Gnanashanmugam, Balalakshmoji Devanand, Rathinasamy Rajakumar

机构信息

Department of Radiodiagnosis, PSG Institute of Medical Sciences and Research, Coimbatore, Tamil Nadu, India.

Department of Neurology, PSG Institute of Medical Sciences and Research, Coimbatore, Tamil Nadu, India.

出版信息

J Neurosci Rural Pract. 2017 Jan-Mar;8(1):135-138. doi: 10.4103/0976-3147.193533.

DOI:10.4103/0976-3147.193533
PMID:28149102
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5225700/
Abstract

Neuromyelitisoptica (NMO) and multiple sclerosis (MS) were once considered to be differing manifestation of same auto immune disease, NMO predominantly involving the optic nerve and cord. Now with discovery of NMO antibody the concept has changed and a spectrum of disorders with lesions in brain has been identified. Occasionally, brain may be the first or the only site of involvement in these disorders hence it is essential to be aware of this spectrum. The brain lesions in NMO/NMOSD may be located in characteristic regions and present with symptoms mimicking non neurological disease. We herein present a case of an adult female who was admitted with intractable vomiting and hiccups; subsequently on MRI brain found to have very tiny demyelinating foci in Area Postrema.

摘要

视神经脊髓炎(NMO)和多发性硬化症(MS)曾被认为是同一种自身免疫性疾病的不同表现形式,NMO主要累及视神经和脊髓。如今,随着NMO抗体的发现,这一概念已发生改变,并且已识别出一系列脑部有病变的疾病。偶尔,脑部可能是这些疾病的首个或唯一受累部位,因此了解这一疾病谱至关重要。NMO/视神经脊髓炎谱系疾病(NMOSD)中的脑部病变可能位于特征性区域,并表现出类似非神经系统疾病的症状。我们在此报告一例成年女性患者,该患者因顽固性呕吐和呃逆入院;随后脑部MRI检查发现最后区有非常微小的脱髓鞘病灶。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b7f9/5225700/bdfc43c90832/JNRP-8-135-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b7f9/5225700/736c4330054c/JNRP-8-135-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b7f9/5225700/f23159f0cafc/JNRP-8-135-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b7f9/5225700/71b858b50825/JNRP-8-135-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b7f9/5225700/bdfc43c90832/JNRP-8-135-g006.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b7f9/5225700/736c4330054c/JNRP-8-135-g003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b7f9/5225700/f23159f0cafc/JNRP-8-135-g004.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b7f9/5225700/71b858b50825/JNRP-8-135-g005.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/b7f9/5225700/bdfc43c90832/JNRP-8-135-g006.jpg

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引用本文的文献

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Commentary.评论
J Neurosci Rural Pract. 2017 Jan-Mar;8(1):138-139. doi: 10.4103/0976-3147.193554.

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