Yassaad Oudrhiri Mohammed, Nabil Raouzi, KacemiInas El, Mohammed Allaoui, Yasser Arkha, Abdessamad El Ouahabi
Neurosurgery Department, Hôpital des Spécialités, UHC Ibn Sina, Rabat, Morocco.
Neuropathology Department, Hôpital des Spécialités, UHC Ibn Sina, Rabat, Morocco.
Pan Afr Med J. 2016 Aug 30;24:334. doi: 10.11604/pamj.2016.24.334.8297. eCollection 2016.
Primary osseous leiomyosarcoma of the spine is a very unusual condition, with only few cases being reported in the literature. In fact, this type of tumors arises from the smooth muscle cells and occurs usually in the uterus and the gastrointestinal tracts. If the spine should be involved, it occurs generally as a metastatic location. Location to the spine as a primary site is exceedingly rare. We present the case of a 37 years old female patient, with multiple spine levels involvement - to vertebral body and to posterior aspects of Vertebra, causing spinal cord compression syndrome. A secondary location to the skull was diagnosed one month later. Through a literature review, we analyze various aspects in the diagnosis and management of this rare entity.
脊柱原发性骨平滑肌肉瘤是一种非常罕见的病症，文献中仅有少数病例报道。事实上，这类肿瘤起源于平滑肌细胞，通常发生于子宫和胃肠道。若脊柱受累，一般是作为转移部位。脊柱作为原发部位极为罕见。我们报告一例37岁女性患者，多个脊柱节段受累——累及椎体及椎骨后方，导致脊髓压迫综合征。一个月后诊断出颅骨为继发部位。通过文献回顾，我们分析了这种罕见疾病在诊断和治疗方面的各个要点。
