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利用光学相干断层扫描技术评估Susac综合征儿科病例中的视网膜变化

Evaluation of Retinal Changes Using Optical Coherence Tomography in a Pediatric Case of Susac Syndrome.

作者信息

Kola Mehmet, Erdöl Hidayet, Ertuğrul Atasoy Sevil, Türk Adem

机构信息

Karadeniz Technical University Faculty of Medicine, Department of Ophthalmology, Trabzon, Turkey.

出版信息

Turk J Ophthalmol. 2017 Jan;47(1):59-62. doi: 10.4274/tjo.27482. Epub 2017 Jan 17.

DOI:10.4274/tjo.27482
PMID:28182173
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5282545/
Abstract

Susac syndrome is a rare occlusive vasculopathy affecting the retina, inner ear and brain. The cause is unknown, although it generally affects young women. This syndrome can be difficult to diagnose because its signs can only be revealed by detailed examination. These signs are not always concomitant, but may appear at different times. This report describes a pediatric case who was diagnosed with Susac syndrome when retinal lesions were identified in the inactive period with the help of optical coherence tomography (OCT). The purpose of this case report is to emphasize the importance of OCT in clarifying undefined retinal changes in Susac syndrome.

摘要

Susac综合征是一种罕见的闭塞性血管病,累及视网膜、内耳和脑。病因不明,尽管该病通常影响年轻女性。这种综合征可能难以诊断,因为其体征只能通过详细检查才能发现。这些体征并非总是同时出现,而是可能在不同时间出现。本报告描述了一例儿科病例,该病例在光学相干断层扫描(OCT)的帮助下,于静止期发现视网膜病变时被诊断为Susac综合征。本病例报告的目的是强调OCT在明确Susac综合征中不明确的视网膜变化方面的重要性。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/053b/5282545/e0eaff5e3b3b/TJO-47-59-g2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/053b/5282545/af7ee8b55527/TJO-47-59-g1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/053b/5282545/e0eaff5e3b3b/TJO-47-59-g2.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/053b/5282545/af7ee8b55527/TJO-47-59-g1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/053b/5282545/e0eaff5e3b3b/TJO-47-59-g2.jpg

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本文引用的文献

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Retinal and choroidal changes and visual outcome in central retinal artery occlusion: an optical coherence tomography study.视网膜中央动脉阻塞时的视网膜和脉络膜变化及视觉预后:一项光学相干断层扫描研究
Am J Ophthalmol. 2015 Apr;159(4):667-76. doi: 10.1016/j.ajo.2015.01.001. Epub 2015 Jan 9.
2
Central retinal artery occlusion and Susac syndrome: a case report.视网膜中央动脉阻塞与苏萨克综合征:一例报告
Retin Cases Brief Rep. 2014 Summer;8(3):187-92. doi: 10.1097/ICB.0000000000000039.
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Susac's syndrome during pregnancy - the first Croatian case.
孕期苏萨克综合征——克罗地亚首例病例。
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Diagnosis and classification of Susac syndrome.Susac 综合征的诊断与分类。
Autoimmun Rev. 2014 Apr-May;13(4-5):347-50. doi: 10.1016/j.autrev.2014.01.038. Epub 2014 Jan 11.
6
Susac syndrome: an Italian case.苏萨克综合征:一例意大利病例。
Neurol Sci. 2013 Dec;34(12):2255-7. doi: 10.1007/s10072-013-1493-7. Epub 2013 Jul 5.
7
Characteristics of Susac syndrome: a review of all reported cases.Susac 综合征的特征:所有报道病例的回顾。
Nat Rev Neurol. 2013 Jun;9(6):307-16. doi: 10.1038/nrneurol.2013.82. Epub 2013 Apr 30.
8
A case of isolated Susac occlusive retinal vasculitis.孤立性 Susac 闭塞性视网膜血管炎 1 例
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Patterns of retinal damage facilitate differential diagnosis between Susac syndrome and MS.视网膜损伤模式有助于苏萨克综合征和 MS 的鉴别诊断。
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Gass plaques and fluorescein leakage in Susac Syndrome.Gass 斑和 Susac 综合征的荧光素渗漏。
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