Department of Pediatric Cardiology, İstanbul Mehmet Akif Ersoy Thoracic and Cardiovascular Surgery Center and Research Hospital, İstanbul, Turkey.
Balkan Med J. 2017 Jan;34(1):71-73. doi: 10.4274/balkanmedj.2015.0535. Epub 2017 Jan 5.
Congenital complete atrioventricular block without any structural heart disease and anti-Ro/La negativity is very rare. Discordant complete atrioventricular block, which is more frequently defined in the literature as an autoimmune mechanism, is much more rare in monozygotic twins.
The 26-year-old healthy mother had given birth in her first spontaneous, uneventful pregnancy to monozygotic twins at week 35. While the first twin's physical examination proved her to be normal with a pulse rate consistent with her age, the second twin had a pulse rate of approximately 40 beats/minute.The patient was confirmed to have congenital complete atrioventricular block.
Despite this case appears to be an isolated one, a discordant complete atrioventricular block regression without any autoimmune evidence should be included in the differential diagnosis of bradycardia in infants.
无任何结构性心脏病且抗 Ro/La 阴性的先天性完全性房室传导阻滞非常罕见。文献中更常定义为自身免疫机制的不一致性完全性房室传导阻滞在同卵双胞胎中则更为罕见。
这位 26 岁的健康母亲在其首次自发性、无并发症的妊娠中于孕 35 周分娩了一对同卵双胞胎。虽然第一胎的体格检查显示其脉搏率与其年龄一致，正常，但第二胎的脉搏率约为 40 次/分钟。该患者被确诊为先天性完全性房室传导阻滞。
尽管本例似乎是孤立的，但在婴儿心动过缓的鉴别诊断中，仍应包括无自身免疫证据的不一致性完全性房室传导阻滞消退。
