Yousaf Farhanah, Spinowitz Bruce, Charytan Chaim, Galler Marilyn
NewYork-Presbyterian/Queens, Flushing, NY, USA.
Case Rep Med. 2017;2017:9410727. doi: 10.1155/2017/9410727. Epub 2017 Feb 6.
A 43-year-old Hispanic male without significant previous medical history was brought to emergency department for syncope following a blood draw to investigate a 40 lbs weight loss during the past 6 months associated with decreased appetite and progressive fatigue. The patient also reported a 1-month history of jaundice. On examination, he was hemodynamically stable and afebrile with pallor and diffuse jaundice but without skin rash or palpable purpura. Normal sensations and power in all extremities were evident on neurological exam. Presence of hemolytic anemia, schistocytosis, thrombocytopenia, and elevated lactate dehydrogenase (LDH) was suggestive of thrombotic thrombocytopenic purpura (TTP). However, presence of leukopenia, macrocytes, and an inadequate reticulocyte response to the degree of anemia served as initial clues to an alternative diagnosis. Two and one units of packed red blood cells were transfused on day 1 and day 3, respectively. In addition, one unit of platelets was transfused on day 2. Daily therapeutic plasma exchange (TPE) was initiated and continued until ADAMTS-13 result ruled out TTP. A low cobalamin (vitamin B12) level was evident at initial laboratory work-up and subsequent testing revealed positive intrinsic factor-blocking antibodies supporting a diagnosis of pernicious anemia with severe cobalamin deficiency. Hematological improvement was observed following vitamin B12 supplementation. The patient was discharged and markedly improved on day 9 with outpatient follow-up for cobalamin supplementation.
一名43岁的西班牙裔男性,既往无重大病史,因在过去6个月内体重减轻40磅,伴有食欲减退和进行性疲劳,在抽血检查后出现晕厥,被送往急诊科。患者还报告有1个月的黄疸病史。体格检查时,他血流动力学稳定,无发热,面色苍白,全身黄疸,但无皮疹或可触及的紫癜。神经系统检查显示四肢感觉和力量正常。存在溶血性贫血、裂体细胞、血小板减少和乳酸脱氢酶(LDH)升高提示血栓性血小板减少性紫癜(TTP)。然而,白细胞减少、大红细胞的存在以及网织红细胞对贫血程度的反应不足是初步诊断为另一种疾病的线索。分别在第1天和第3天输注了2单位和1单位的浓缩红细胞。此外,在第2天输注了1单位血小板。开始每日进行治疗性血浆置换(TPE),并持续进行,直到ADAMTS-13结果排除TTP。在初始实验室检查中发现钴胺素(维生素B12)水平较低,随后的检测显示内因子阻断抗体呈阳性,支持恶性贫血伴严重钴胺素缺乏的诊断。补充维生素B12后观察到血液学改善。患者于第9天出院,门诊随访补充钴胺素,病情明显好转。