Nacaroğlu Hikmet Tekin, Ünsal-Karkıner Canan Şule, Bahçeci-Erdem Semiha, Özdemir Rahmi, Karkıner Aytaç, Alper Hüdaver, Can Demet
Divisions of Pediatric Allergy, Dr Behçet Uz Children's Hospital, İzmir, Turkey.
Divisions of Pediatric Cardiology, Dr Behçet Uz Children's Hospital, İzmir, Turkey.
Turk J Pediatr. 2016;58(3):337-342. doi: 10.24953/turkjped.2016.03.020.
Congenital pulmonary vascular abnormalities arise from several etiologies. These anomalies are difficult to categorize and sorted into distinct classifications. Major pulmonary vascular abnormalities can be ranked as interruption of the main pulmonary artery or its absence, emergence of the left pulmonary artery in the right pulmonary artery, pulmonary venous drainage abnormalities, and pulmonary arteriovenous malformations (PAVMs). Some of the cases are asymptomatic and diagnosed by coincidence, whereas a few of them are diagnosed by typical findings in the newborn and infancy period, symptoms, and radiological appearances. Early diagnosis is important, since death may occur as a result of pulmonary and cardiac pathologies developed in patients with pulmonary vascular anomalies. In this case presentation, the clinical and radiological findings of patients that presented with different complaints and were diagnosed with pulmonary vascular anomalies were introduced.
先天性肺血管异常由多种病因引起。这些异常难以分类并归入不同类别。主要的肺血管异常可列为肺动脉主干中断或缺失、左肺动脉发自右肺动脉、肺静脉引流异常以及肺动静脉畸形（PAVM）。部分病例无症状，偶然被诊断出来，而少数病例则在新生儿期和婴儿期通过典型表现、症状及影像学特征得以诊断。早期诊断很重要，因为患有肺血管异常的患者可能因肺部和心脏病变而死亡。在本病例报告中，介绍了因不同症状就诊并被诊断为肺血管异常的患者的临床和影像学表现。
