Perna Gian Piero, Gini Guido, Brambatti Michela, Battistoni Ilaria, Marini Marco, Angelini Luca, Francioni Matteo, Goteri Gaia, Dottori Melissa
Divisione di Cardiologia, Dipartimento Cardiovascolare, Ospedali Riuniti di Ancona, Ancona.
Clinica di Ematologia, Università Politecnica delle Marche, Ospedali Riuniti di Ancona, Ancona.
G Ital Cardiol (Rome). 2017 Jan;18(1):7-10. doi: 10.1714/2628.27021.
Primitive cardiac lymphoma (PCL) is a rare disease accounting for only 1-2% of primary cardiac tumors. Diffuse large B cell lymphoma is the most common type and shows a rapid progression with poor prognosis. The clinical presentation of PCL is nonspecific, and echocardiographic study is essential to the initial work-up. Magnetic resonance imaging and computed tomography scan are the methods of choice for the assessment of tumor extension. The definitive diagnosis is histopathology examination. Chemotherapy and radiotherapy represent the best treatment and should be started promptly after PCL diagnosis. We here report a case of PCL in a 59-year-old man complicated by pulmonary microembolism, atrial fibrillation and signs of right outflow tract obstruction.
原发性心脏淋巴瘤(PCL)是一种罕见疾病,仅占原发性心脏肿瘤的1%-2%。弥漫性大B细胞淋巴瘤是最常见的类型,进展迅速,预后较差。PCL的临床表现不具有特异性,超声心动图检查对于初始检查至关重要。磁共振成像和计算机断层扫描是评估肿瘤扩散的首选方法。确诊依靠组织病理学检查。化疗和放疗是最佳治疗方法,应在PCL确诊后立即开始。我们在此报告一例59岁男性的PCL病例,该病例并发肺微栓塞、心房颤动及右心室流出道梗阻体征。