Sultan Fateh Ali Tipoo, Ahmed Mehnaz Atiq, Miller Jamie, Selvanayagam Joseph B
Aga Khan University Hospital, Karachi, aPakistan.
Flinders University, Adelaide, fAustralia.
J Saudi Heart Assoc. 2017 Apr;29(2):139-142. doi: 10.1016/j.jsha.2016.08.001. Epub 2016 Aug 24.
Arrhythmogenic right ventricular cardiomyopathy (ARVC) is seldom recognized clinically in infancy or under the age of 10. We report a case of a 9-year-old girl with ARVC, who presented with signs and symptoms of heart failure and palpitations. Holter monitoring showed frequent premature ventricular beats and echocardiogram revealed dilated and dysfunctional right ventricle with normal tricuspid valve and no evidence of intracardiac shunt. Cardiac magnetic resonance showed classical features of ARVC with both ventricular involvements. After optimization of medical treatment the patient was referred for ICD implantation.
致心律失常性右室心肌病（ARVC）在婴儿期或10岁以下儿童中临床少见。我们报告一例9岁患ARVC的女孩，她表现出心力衰竭和心悸的症状与体征。动态心电图监测显示频发室性早搏，超声心动图显示右心室扩张且功能障碍，三尖瓣正常，无心脏内分流证据。心脏磁共振显示ARVC的典型特征，累及双心室。在优化药物治疗后，患者被转诊进行植入式心律转复除颤器（ICD）植入。
