Okui Masayuki, Yamamichi Takashi, Asakawa Ayaka, Harada Masahiko, Horio Hirotoshi
Department of Thoracic Surgery, Tokyo Metropolitan Cancer and Infectious Diseases Center Komagome Hospital.
Korean J Thorac Cardiovasc Surg. 2017 Apr;50(2):119-122. doi: 10.5090/kjtcs.2017.50.2.119. Epub 2017 Apr 5.
Pure red cell aplasia (PRCA) and hypogammaglobulinemia are paraneoplastic syndromes that are rarer than myasthenia gravis in patients with thymoma. Good syndrome coexisting with PRCA is an extremely rare pathology. We report the case of a 50-year-old man with thymoma and PRCA associated with Good syndrome who achieved complete PRCA remission after thymectomy and postoperative immunosuppressive therapy, and provide a review of the pertinent literature.
纯红细胞再生障碍性贫血(PRCA)和低丙种球蛋白血症是胸腺瘤患者中比重症肌无力更罕见的副肿瘤综合征。与PRCA共存的古德综合征是一种极其罕见的病理情况。我们报告一例50岁男性胸腺瘤合并与古德综合征相关的PRCA患者,该患者在胸腺切除术后及术后免疫抑制治疗后PRCA完全缓解,并对相关文献进行综述。