Hohenforst-Schmidt Wolfgang, Grapatsas Konstantinos, Dahm Manfred, Zarogoulidis Paul, Leivaditis Vasileios, Kotoulas Christophoros, Tomos Periclis, Koletsis Efstratios, Tsilogianni Zoi, Benhassen Naim, Huang Haidong, Kosmidis Christoforos, Kosan Bora
Sana Clinic Group Franken, Department of Cardiology/Pulmonology/Intensive Care/Nephrology, "Hof" Clinics, University of Erlangen, Hof, Germany.
Department of Cardiothoracic and Vascular Surgery, Westpfalz Klinikum, Academic Educational Hospital, Heidelberg University and Mainz University, Kaiserslautern, Germany.
Respir Med Case Rep. 2017 Apr 12;21:99-104. doi: 10.1016/j.rmcr.2017.04.007. eCollection 2017.
Solitary Fibrous Tumor of the Pleura (SFTP) is a rare tumor of the pleura. Worldwide about 800 patients diagnosed with this oncological entity have been described in the existing literature. We report our center's 13 year experience. During this time three patients suffering from this rare disease have been treated in our department. All patients were asymptomatic and their diagnosis was initially triggered by a random finding in a routine chest x-ray. The diagnosis was set preoperatively through a needle biopsy under computer tomography (CT) guidance. The tumors were resected surgically though video-assisted thoracoscopic surgery (VATS) or thoracotomy. Because of the lack of specific guidelines due to the rarity of the disease a long-term, systematic follow-up was recommended and performed. Parallel an overview of the diagnostic and therapeutic procedures of the rare tumor is made.
胸膜孤立性纤维瘤(SFTP)是一种罕见的胸膜肿瘤。在现有文献中,全世界约有800例被诊断为此种肿瘤实体的患者。我们报告我们中心13年的经验。在此期间,我们科室治疗了3例患有这种罕见疾病的患者。所有患者均无症状,其诊断最初是由常规胸部X光检查中的偶然发现引发的。通过计算机断层扫描(CT)引导下的针吸活检在术前确定诊断。通过电视辅助胸腔镜手术(VATS)或开胸手术对肿瘤进行手术切除。由于该疾病罕见,缺乏具体指南,因此建议并进行了长期、系统的随访。同时,对这种罕见肿瘤的诊断和治疗程序进行了概述。