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严重获得性血管性血友病综合征患者围手术期静脉注射免疫球蛋白治疗：病例报告及文献复习

Perioperative intravenous immunoglobulin treatment in a patient with severe acquired von Willebrand syndrome: case report and review of the literature.

作者信息

Jennes Eva, Guggenberger Dorothee, Zotz Rainer, Thompson Lora, Brümmendorf Tim H, Koschmieder Steffen, Jost Edgar

机构信息

Department of Hematology, Oncology, Hemostaseology and Stem Cell Transplantation Medical Faculty RWTH Aachen University Aachen Germany.

Praxis W8 Aachen Germany.

出版信息

Clin Case Rep. 2017 Mar 30;5(5):664-670. doi: 10.1002/ccr3.890. eCollection 2017 May.

DOI:10.1002/ccr3.890
PMID:28469872
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5412814/
Abstract

Acquired von Willebrand syndrome may be related to plasma cell dyscrasia and can cause severe bleeding complications. Treatment, for example, with intravenous immunoglobulins may be indicated in selected cases. Physicians treating plasma cell dyscrasia have to be aware of bleeding complications in these patients, and clarification is necessary.

摘要

获得性血管性血友病综合征可能与浆细胞异常增殖有关，并可导致严重的出血并发症。例如，在某些情况下可能需要使用静脉注射免疫球蛋白进行治疗。治疗浆细胞异常增殖的医生必须意识到这些患者存在出血并发症，对此进行明确诊断很有必要。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d5af/5412814/649c6ef03fde/CCR3-5-664-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d5af/5412814/304a144ada4a/CCR3-5-664-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d5af/5412814/649c6ef03fde/CCR3-5-664-g002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d5af/5412814/304a144ada4a/CCR3-5-664-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/d5af/5412814/649c6ef03fde/CCR3-5-664-g002.jpg

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Ann Hematol. 2016 May;95(6):945-57. doi: 10.1007/s00277-016-2650-x. Epub 2016 Apr 4.
2
Diagnosis, prevention, and management of bleeding episodes in Philadelphia-negative myeloproliferative neoplasms: recommendations by the Hemostasis Working Party of the German Society of Hematology and Medical Oncology (DGHO) and the Society of Thrombosis and Hemostasis Research (GTH).费城阴性骨髓增殖性肿瘤出血事件的诊断、预防及管理：德国血液学与医学肿瘤学会（DGHO）及血栓形成与止血研究学会（GTH）止血工作组的建议
Ann Hematol. 2016 Apr;95(5):707-18. doi: 10.1007/s00277-016-2621-2. Epub 2016 Feb 26.
3
Treatment of the acquired von Willebrand syndrome.
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