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囊性纤维化患者的复杂性局限性皮肤血管炎:病例系列

complex and limited cutaneous vasculitis in patients with cystic fibrosis: a case series.

作者信息

Kayria Muttardi, Chris Orchard, Dhasmana Devesh J, Nilesh Morar, Hodson Margaret E, Khin Gyi, Diana Bilton, Simmonds Nicholas J

机构信息

Department of Cystic Fibrosis, Royal Brompton Hospital, London SW3 6NP, UK.

Department of Dermatology, Royal Free Hospital, London NW3 2QG, UK.

出版信息

JRSM Open. 2017 Apr 3;8(4):2054270417692732. doi: 10.1177/2054270417692732. eCollection 2017 Apr.

DOI:10.1177/2054270417692732
PMID:28491333
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC5405907/
Abstract

There is a high association of reactive skin presentations, mainly limited cutaneous vasculitis in patients with cystic fibrosis and complex chronic infection. This may be due to raised levels of circulating inflammatory mediators.

摘要

在囊性纤维化和复杂慢性感染患者中,反应性皮肤表现(主要是局限性皮肤血管炎)的关联性很高。这可能是由于循环炎症介质水平升高所致。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ca19/5405907/2de7cd9e8d35/10.1177_2054270417692732-fig1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ca19/5405907/2de7cd9e8d35/10.1177_2054270417692732-fig1.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/ca19/5405907/2de7cd9e8d35/10.1177_2054270417692732-fig1.jpg

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本文引用的文献

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Cystic fibrosis: what to expect now in the early adult years.囊性纤维化:在成年早期的预期。
Paediatr Respir Rev. 2012 Dec;13(4):206-14. doi: 10.1016/j.prrv.2012.03.005. Epub 2012 Jun 9.
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Treatment of cystic fibrosis associated cutaneous vasculitis with chloroquine.氯喹治疗囊性纤维化相关性皮肤血管炎。
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Cureus. 2020 May 16;12(5):e8158. doi: 10.7759/cureus.8158.
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J Cyst Fibros. 2004 Aug;3(3):179-83. doi: 10.1016/j.jcf.2004.04.005.
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Outcome for patients colonised with Burkholderia cepacia in a Birmingham adult cystic fibrosis clinic and the end of an epidemic.伯明翰成人囊性纤维化诊所中感染洋葱伯克霍尔德菌患者的治疗结果及疫情终结
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Vasculitis and arthropathy in cystic fibrosis.囊性纤维化中的血管炎和关节病。
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