Kim Jae-Young, Jung Tae-Young, Lee Kyung-Hwa, Kim Seul-Kee
Department of Neurosurgery, Chonnam National University Medical School, Chonnam National University Hwasun Hospital, Hwasun, Korea.
Department of Pathology, Chonnam National University Medical School, Chonnam National University Hwasun Hospital, Hwasun, Korea.
Brain Tumor Res Treat. 2017 Apr;5(1):37-41. doi: 10.14791/btrt.2017.5.1.37. Epub 2017 Apr 30.
We report a rare case of subependymal giant cell astrocytoma (SEGA) associated with tumoral bleeding in a pediatric patient without tuberous sclerosis complex (TSC). A 10-year-old girl presented with a 2-week history of an increasingly aggravating headache. Brain magnetic resonance imaging revealed an approximately 3.6-cm, well-defined, heterogeneously enhancing mass with multistage hemorrhages on the right-sided foramen of Monro. The tumor was completely resected using a transcallosal approach. Intraoperatively, the mass presented as a gray-colored firm tumor associated with acute and subacute hemorrhages. The origin of the mass was identified as the ventricular septum adjacent to the foramen of Monro. A pathological analysis revealed pleomorphic multinucleated eosinophilic tumor cells with abundant cytoplasm. These cells showed positive staining for the glial fibrillary acidic protein and S100 protein. A diagnosis of SEGA was established. The patient recovered without any neurological symptoms. There was no evidence of TSC. The radiological follow-up showed no recurrence for 2 years. This was a case of SEGA with intratumoral hemorrhage, for which a favorable outcome was achieved, without any neurological deficit after tumoral resection.
我们报告了一例罕见的室管膜下巨细胞星形细胞瘤(SEGA),该病例发生在一名无结节性硬化症(TSC)的儿科患者中,并伴有肿瘤出血。一名10岁女孩出现了持续2周且日益加重的头痛症状。脑部磁共振成像显示,在右侧孟氏孔处有一个大小约为3.6厘米、边界清晰、强化不均匀且伴有多阶段出血的肿块。采用经胼胝体入路将肿瘤完全切除。术中,肿块表现为一个灰白色的实性肿瘤,伴有急性和亚急性出血。肿块起源于邻近孟氏孔的室间隔。病理分析显示有多形性多核嗜酸性肿瘤细胞,胞质丰富。这些细胞胶质纤维酸性蛋白和S100蛋白染色呈阳性。确诊为SEGA。患者康复,无任何神经症状。没有TSC的证据。影像学随访显示2年内无复发。这是一例伴有肿瘤内出血的SEGA病例,肿瘤切除后未出现任何神经功能缺损,取得了良好的治疗效果。